- Onset within first two years of life
- Severe Lymphedema onset at birth or as infant
- Milroy's Disease is a famial subtype
-
Lower Extremity Edema
- Right leg more often affected
- Bilateral involvement in 25% of cases
- Involves foot dorsum up to knee
- Swelling of external genitalia
- Intestinal lymphangiectasia, Protein-losing Enteropathy
- Cystic Hygroma
- Pulmonary lymphangiectasia
- Sabiston (1997) Surgery, Saunders, p.1574-5
- Rockson (2001) Am J Med 110:288-95 [PubMed]