- Lymphangioma
- Benign tumor developing as a Congenital Abnormality of the lymph system
- Results in dilated lymph channels
- Onset under age 2 years (typically as a young infant)
- Turner's Syndrome
- Noonan's Syndrome
- Down Syndrome
- Initial
- Asymptomatic
- Painless lesion unless infected or bleeding
- Progression: Continues to increases in size
- 90% symptomatic by age 2 years
- Fluctuant mass usually in neck
- Mass transilluminates
- Infection
- Bleeding
- Airway compromise (due to compression)
-
Chest XRay
- Identify mediastinal extension
- Pleural Effusion
- Deliver where NICU available if diagnosed prenatally
- Risk of airway compromise
- Surgical excision
- Recurrence rate after surgical excision: 10-15%
- Townsend (2001) Sabiston Surgery, Saunders, p. 546-7
- Muensterer (2000) Pediatr Rev 21(4):139-43 [PubMed]
- Weintraub (2000) Otolaryngol Clin North Am 33:1171-89 [PubMed]