Cerebellum

Chiari II Malformation

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Chiari II Malformation, Arnold-Chiari Malformation, Arnold Chiari II Malformation

  • See Also
  1. Chiari I Malformation
  2. Dysraphism
  • Definition
  • Chiari II Malformation
  1. Cerebellum and Brain Stem elongate via foramen magnum
  2. Cerebellar Tonsils dip into foramen magnum
    1. Risk of cord injury with even minor Trauma
  • Presentation
  1. Presentation as infant (10% of cases)
    1. Apnea
    2. Weak cry
    3. Stridor
      1. Emergency - may herald Respiratory Failure
  2. Insidious course during childhood
    1. Gait Abnormality
    2. Spasticity
    3. Incoordination
  • Associated Conditions
  1. Myelomeningocele
  2. Hydrocephalus
  3. Corpus callosum abnormalities
  • Management
  1. Management of Myelomeningocele and Hydrocephalus
  2. Decompression of at foramen magnum may be indicated
  • Precautions
  1. Acute conditions indicating emergent MRI
    1. Head or neck Trauma (even minor Trauma)
    2. Stridor (may herald Respiratory Failure)
  • References
  1. Majoewsky (2012) EM:Rap-C3 2(9): 5
  2. Behrman (2000) Nelson Pediatrics, Saunders, p. 1810
  3. Goldman (2000) Cecil Medicine, Saunders, p. 2076