- Congenital or develops in early childhood
- Hyperpigmentation from increased Melanin deposition
- Often present at birth
- Isolated lesions are common (present in up to 10-30% of the population)
- Asymptomatic
- "Coffee with milk" (tan to brown) colored flat Macule
- Usually located on trunk
- Size varies from <4 cm in infants to 20-30 cm in adults
- Criteria to consider associated congenital conditions below
- Six or more lesions that meet size criteria
- Size criteria
- Prepubertal: Lesions 5 mm or larger
- Postpubertal: Lesions 15 mm or larger
- Neurofibromatosis
- Tuberous Sclerosis
- Albright Syndrome
- Fanconi Anemia
- None needed
- Consider treatment only for cosmetic reasons
- Laser therapy
- Surgical excision