- Most common in 40 to 50 year old women
- Neuroendocrine tumor arising from from glomus bodies
- Jugular bulb origin or
- Middle ear neural plexus
- Tympanic Membrane invasion follows Hearing Loss
- May involve Cranial Nerves
- Pulsating Tinnitus
- Hearing Loss
- Dark blue, purple or red-blue mass behind TM
- Anomalous Carotid Artery
- Anomalous jugular bulb
- Do not biopsy (very vascular)
- Surgical excision