- Does not contain nevus cells
- Onset in teen boys
- Becker's Nevus Syndrome
- Skin lesion with Smooth Muscle fiber abnormalities
- Breast hypoplasia (unilateral)
- Limb hypoplasia (unilateral)
- Scoliosis
- Spina Bifida Occulta
- No risk of malignancy
- Habif (2003) Clinical Dermatology, 4th ed.. Mosby, p. 773-813