Peds

Aplasia Cutis Congenita

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Aplasia Cutis Congenita

  • See Also
  1. Newborn Skin Exam
  • Epidemiology
  1. Incidence: 0.03% of newborns
  • Pathophysiology
  1. Congenital absence of skin
  2. Embryonic defect present in a small subset of patients
  • Signs
  1. Bulla, ulceration or atrophic lesion
  • Distribution
  1. Most often at the scalp near the vertex
  • Labs
  1. Biopsy shows absent Dermis or Epidermis
  • Management
  1. Avoid secondary Bacterial Infection
  2. Surgical excision in some cases