• See Also
  1. Bullous Disease
  2. Linear IgA Dermatosis
  3. Henoch-Schonlein Purpura (IgA Vasculitis)
  • Epidemiology
  1. Rare
  2. Age of Onset: Under age 5 years
  • Pathophysiology
  1. Autoimmune bullous disorder
  2. Variant of Linear IgA Dermatosis (seen in adults)
  • Symptoms
  1. Pruritus and burning Sensation
  • Signs
  1. Sudden onset of tense inflamed Blisters over red base
    1. May appear as collarettes of Blisters
  2. Distribution
    1. Most commonly found on genitalia
    2. Also may involves face and perioral skin
    3. Oral Mucosa involved in 50% of cases
  • Labs
  1. Same as Linear IgA Dermatosis
  • Management
  1. Same as Linear IgA Dermatosis
  • Course
  1. Resolves within 2 years of onset in most cases
  • References
  1. Bickle (2002) Am Fam Physician 65(9):1861-70 [PubMed]
  2. Cotell (2000) Am J Emerg Med 18(3):288-99 [PubMed]